Huge retroperitoneal epithelioid angiomyolipoma: A case report
نویسندگان
چکیده
Angiomyolipoma (AML) is a type of tumor in the perivascular epithelioid cell neoplasm (PEComa) family. Epithelioid angiomyolipoma (EAML), having malignant potential, is considered a rare variant of angiomyolipoma. The most common site of EAMLs is kidney, and extra-renal EAMLs are very uncommon, with liver being the most common site.1 Other locations including retroperitoneum, uterus, liver, lung, breast, cardiac septum, pancreas, prostate, and gastrointestinal tract have also been described.2 To our acknowledgment, only 6 cases of retroperitoneal EAML was reported in the English literature.3 Presented here is a 46-year-old female with a giant (20 cm 15 cm x 15cm) retroperitoneal epithelioid angiomyolipoma.
منابع مشابه
Wünderlich syndrome from a malignant epithelioid angiomyolipoma.
Received August 2008 Accepted December 2008 INTRODUCTION Angiomyolipoma of the kidney has classically been considered as a tumor of the connective tissue composed of fat, vascular tissue, and smooth muscle. In most cases, it is a tumor with benign behavior that may appear sporadically or associated with tuberous sclerosis syndrome. Macroscopically, these tumors are greyish yellow in color, and ...
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